Pediatric EMG Cases-Dr. Ginsberg Presentation

Dr. Ginsberg Presentation

Pdf Summary

The document outlines the presentation of Dr. Matt Ginsberg, MD, on the topic of monomelic amyotrophy at a 2024 conference. The medical history highlights a 17-year-old male experiencing dizzy spells and left hand weakness, with a background of progressive hand weakness, tremors, migraines, and other neurological symptoms over two years. The examination reveals atrophy and tremors, but normal sensory response and downgoing plantar reflexes. <br /><br />The differential diagnosis considered includes conditions like juvenile ALS and other structural myelopathies. The recommended diagnostic and assessment tools include EMG for C7-T1 myotomal involvement and dynamic MRI with dural displacement. Potential treatments discussed are conservative management with neck collars and surgical options like anterior fusion or posterior duraplasty.<br /><br />The presentation suggests monomelic amyotrophy, defined by asymmetric and chronic progressive weakness mainly in hand and forearm muscles, predominantly occurring in young males. This condition can exhibit intervals of stability and intermittent progression over years, occasionally accompanied by sensory symptoms. The pathophysiology may involve disproportionate cervical growth affecting the dura, causing local ischemia or compression.<br /><br />The document also encourages attendees to use the AANEM app for feedback and details how attendees can claim educational credits post-conference. For monitoring progress, tools such as MUNE/MUNIX and handheld dynamometry are mentioned along with references to supporting research.

Keywords

Monomelic Amyotrophy

Dr. Matt Ginsberg

Neurological Symptoms

Differential Diagnosis

Juvenile ALS

EMG

Cervical Myelopathy

Treatment Options

Pathophysiology

AANEM Conference

electromyography